Anti-AUH antibody (ab107173)

Overview

• Product nameAnti-AUH antibodySee all AUH primary antibodies ...
• Description
  Rabbit polyclonal to AUH
• Tested applicationsWB more details
• Species reactivity
  Reacts with: Human
  
• Immunogen

  KLH conjugated synthetic peptide corresponding to a region within C terminal amino acids 320-339 of Human AUH (NP_001689.1).

• Positive controlHepG2 cell line lysate

Properties

• FormLiquid
• Storage instructionsStore at 4°C (up to 6 months). For long term storage store at -20°C
• Storage bufferPreservative: 0.09% Sodium Azide
  Constituents: PBS
• Concentration information loading...
• PurityImmunogen affinity purified
• Purification notesab107173 is purified through a protein A column, followed by peptide affinity purification.
• Clonality Polyclonal
• IsotypeIgG
• Research Areas
  • Metabolism
  • Pathways and Processes
  • Metabolic signaling pathways
  • Nucleotide metabolism

  • Metabolism
  • Pathways and Processes
  • Mitochondrial Metabolism
  • Mitochondrial markers

  • Metabolism
  • Types of disease
  • Cancer

  • Metabolism
  • Pathways and Processes
  • Metabolic signaling pathways
  • Amino acid metabolism

  • Signal Transduction
  • Metabolism
  • Mitochondrial

  • Signal Transduction
  • Metabolism
  • Amino Acids

  • Tags & Cell Markers
  • Subcellular Markers
  • Organelles
  • Mitochondria

  • Epigenetics and Nuclear Signaling
  • Chromatin Binding Proteins
  • DNA / RNA binding

Applications

Target

• RelevanceAUH (3-methylglutaconyl-CoA hydratase) catalyzes the conversion of 3-methylglutaconyl-CoA to 3-hydroxy-3-methylglutaryl-CoA and has very low enoyl-CoA hydratase activity. Deletion or mutation of the AUH gene causes the metabolic disease 3-methylglutaconic aciduria type I (MGA1). MGA type I is characterized by an abnormal organic acid profile in which there is excessive urinary excretion of 3-methylglutaconic acid, 3-methylglutaric acid and 3-hydroxyisovaleric acid. AUH is also an RNA-binding protein that binds in vitro to clustered 5'-AUUUA-3' motifs.
• Cellular localizationMitochondrial
• Database links
  • Entrez Gene: 549 Human
  • Omim: 600529 Human
  • SwissProt: Q13825 Human
  • Unigene: 175905 Human

• Alternative names
  3 methylglutaconyl CoA hydratase antibody7371-1 antibodyAU binding protein/enoyl CoA hydratase antibody

  AU RNA binding protein/enoyl CoA hydratase antibodyAU RNA binding protein/enoyl Coenzyme A hydratase antibodyAU specific RNA binding antibodyAU specific RNA binding enoyl CoA hydratase antibodyCat.#: 7371-1 antibodyEpitomics antibodyMethylglutaconyl CoA hydratase antibodyMethylglutaconyl CoA hydratase mitochondrial antibodyMGA Type I antibodyRabMab antibody

  see all

Anti-AUH antibody images

• 

  Western blot - AUH antibody (ab107173)
  Anti-AUH antibody (ab107173) at 1/100 dilution + HepG2 cell line lysate at 35 µg
  
  Predicted band size : 36 kDa