Overview

  • Product nameAnti-MCCC1 antibody
    See all MCCC1 primary antibodies
  • Description
    Mouse monoclonal to MCCC1
  • Tested applicationsSuitable for: WBmore details
  • Species reactivity
    Reacts with: Human
  • Immunogen

    Recombinant fragment: FTLQAHDQFS PFSSSSGRRL NISYTRNMTL KDGKNNVAIA VTYNHDGSYS MQIEDKTFQV LGNLYSEGDC TYLKCSVNGV ASKAKLIILE NTIYLFSKEG , corresponding to amino acids 526-626 of Human MCCC1

Properties

Applications

Our Abpromise guarantee covers the use of ab57500 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

Application Abreviews Notes
WB
  • Application notesWB: Use at a concentration of 1-5 µg/ml.

    This antibody has only been tested in WB against the recombinant fragment used as immunogen. We have no data on the detection of endogenous protein.

    Not yet tested in other applications.
    Optimal dilutions/concentrations should be determined by the end user.
  • Target

    • RelevanceMCCC1 is the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Defects in MCCC1 are the cause of methylcrotonoyl-CoA carboxylase deficiency type 1 (MCC1 deficiency). MCC1 deficiency is an autosomal recessive disorder of leucine catabolism.
    • Cellular localizationMitochondrion matrix.
    • Database links
    • Alternative names
      • 3-methylcrotonyl-CoA carboxylase 1 antibody
      • 3-methylcrotonyl-CoA carboxylase biotin-containing subunit antibody
      • 3-methylcrotonyl-CoA carboxylase, alpha antibody
      • 3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha antibody
      • DKFZp686B20267 antibody
      • FLJ25545 antibody
      • MCC-B antibody
      • MCCA antibody
      • MCCase subunit alpha antibody
      • methylcrotonoyl-CoA carboxylase 1 (alpha) antibody
      • methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial antibody
      • methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) antibody
      see all

    Anti-MCCC1 antibody images

    • Western blot against tagged recombinant protein immunogen using ab57500 MCCC1 antibody at 1ug/ml. Predicted band size of immunogen is 37 kDa

    References for Anti-MCCC1 antibody (ab57500)

    ab57500 has not yet been referenced specifically in any publications.

    Product Wall

    There are currently no Abreviews or Questions for ab57500.
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    Please note: All products are "FOR RESEARCH USE ONLY AND ARE NOT INTENDED FOR DIAGNOSTIC OR THERAPEUTIC USE"