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ACAA2

Function

In the production of energy from fats, this is one of the enzymes that catalyzes the last step of the mitochondrial beta-oxidation pathway, an aerobic process breaking down fatty acids into acetyl-CoA (Probable). Using free coenzyme A/CoA, catalyzes the thiolytic cleavage of medium- to long-chain unbranched 3-oxoacyl-CoAs into acetyl-CoA and a fatty acyl-CoA shortened by two carbon atoms (Probable). Also catalyzes the condensation of two acetyl-CoA molecules into acetoacetyl-CoA and could be involved in the production of ketone bodies (Probable). Also displays hydrolase activity on various fatty acyl-CoAs (PubMed:25478839). Thereby, could be responsible for the production of acetate in a side reaction to beta-oxidation (Probable). Abolishes BNIP3-mediated apoptosis and mitochondrial damage (PubMed:18371312).

Pathway

Lipid metabolism; fatty acid beta-oxidation.

Sequence similarities

Belongs to the thiolase-like superfamily. Thiolase family.

Cellular localization

  • Mitochondrion

Alternative names

  • Acetyl-CoA acetyltransferase
  • Acetyl-CoA acyltransferase
  • Beta-ketothiolase
  • Mitochondrial 3-oxoacyl-CoA thiolase
  • T1
  • ACAA2

Target type

Proteins

Molecular weight

41924Da