Arsa
Function
Hydrolyzes cerebroside sulfate.
Post-translational modifications
The conversion to 3-oxoalanine (also known as C-formylglycine, FGly), of a serine or cysteine residue in prokaryotes and of a cysteine residue in eukaryotes, is critical for catalytic activity. This post-translational modification is severely defective in multiple sulfatase deficiency (MSD).
Sequence Similarities
Belongs to the sulfatase family.
Cellular localization
- Endoplasmic reticulum
- Lysosome
Alternative names
As2, Arsa, Arylsulfatase A, ASA, Cerebroside-sulfatase