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Function

Beta-1,4-galactosyltransferase 1

The Golgi complex form catalyzes the production of lactose in the lactating mammary gland and could also be responsible for the synthesis of complex-type N-linked oligosaccharides in many glycoproteins as well as the carbohydrate moieties of glycolipids.

Processed beta-1,4-galactosyltransferase 1

The cell surface form functions as a recognition molecule during a variety of cell to cell and cell to matrix interactions, as those occurring during development and egg fertilization, by binding to specific oligosaccharide ligands on opposing cells or in the extracellular matrix.

Involvement in disease

Congenital disorder of glycosylation 2D

CDG2D

A multisystem disorder caused by a defect in glycoprotein biosynthesis and characterized by under-glycosylated serum glycoproteins. Congenital disorders of glycosylation result in a wide variety of clinical features, such as defects in the nervous system development, psychomotor retardation, dysmorphic features, hypotonia, coagulation disorders, and immunodeficiency. The broad spectrum of features reflects the critical role of N-glycoproteins during embryonic development, differentiation, and maintenance of cell functions.

None

The disease is caused by variants affecting the gene represented in this entry.

Combined low LDL and fibrinogen

CLDLFIB

An autosomal recessive condition characterized by low plasma LDL-cholesterol and fibrinogen levels, and associated with a decreased risk of coronary artery disease.

None

Disease susceptibility may be associated with variants affecting the gene represented in this entry.

Pathway

Protein modification; protein glycosylation.

Post-translational modifications

The soluble form derives from the membrane forms by proteolytic processing.

Sequence similarities

Belongs to the glycosyltransferase 7 family.

Tissue specificity

Ubiquitously expressed, but at very low levels in fetal and adult brain.

Cellular localization

  • Isoform Long
  • Golgi apparatus
  • Golgi stack membrane
  • Single-pass type II membrane protein
  • Cell membrane
  • Single-pass type II membrane protein
  • Cell surface
  • Cell projection
  • Filopodium
  • Found in trans cisternae of Golgi but is mainly localized at the plasma membrane (PubMed:1714903). B4GALT1 cell surface expression is regulated by UBE2Q1 (By similarity).
  • Isoform Short
  • Golgi apparatus
  • Golgi stack membrane
  • Single-pass type II membrane protein
  • Found in trans cisternae of Golgi.
  • Processed beta-1,4-galactosyltransferase 1
  • Secreted
  • Soluble form found in body fluids.

Alternative names

GGTB2, B4GALT1, Beta4Gal-T1, b4Gal-T1, Lactose synthase A protein, N-acetyllactosamine synthase, Nal synthase

Target type

Proteins

Primary research area

Immunology & Infectious Disease

Molecular weight

43920Da

We found 5 products in 4 categories

Primary Antibodies

Target

Application

Reactive species

Assay Kits

Target

Reactive species

Detection method

Proteins & Peptides

Target

Species of origin

Cell Lines & Lysates

Target

Cell type

Species or organism