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Function

Catalyzes the formation of L-carnitine from gamma-butyrobetaine.

Pathway

Amine and polyamine biosynthesis; carnitine biosynthesis.

Sequence similarities

Belongs to the gamma-BBH/TMLD family.

Tissue specificity

Highly expressed in kidney; moderately expressed in liver; very low expression in brain.

Cellular localization

  • Cytoplasm

Alternative names

BBH, BBOX, BBOX1, Gamma-butyrobetaine dioxygenase, Gamma-butyrobetaine hydroxylase, Gamma-BBH

Target type

Proteins

Primary research area

Metabolism

Molecular weight

44715Da

We found 2 products in 1 category

Primary Antibodies

Target

Application

Reactive species

Search our catalogue for 'BBOX1' (2)

Products

ab171959

Anti-BBOX1 antibody [EPR11309]

Recombinant
RabMAb