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CCDC8

Domain

The PxLPxI/L motif mediates interaction with ankyrin repeats of ANKRA2.

Function

Core component of the 3M complex, a complex required to regulate microtubule dynamics and genome integrity. It is unclear how the 3M complex regulates microtubules, it could act by controlling the level of a microtubule stabilizer (PubMed:24793695, PubMed:24793696). Required for localization of CUL7 to the centrosome (PubMed:24793695).

Involvement in disease

3M syndrome 3

3M3

A disorder characterized by poor postnatal growth and distinctive facial features, including triangular facies, frontal bossing, fleshy tipped nose, and fleshy lips. Other features may include skeletal anomalies and prominent heels.

None

The disease is caused by variants affecting the gene represented in this entry.

Tissue specificity

Widely expressed with low levels in spleen, skeletal muscle, small intestine, kidney and liver.

Cellular localization

  • Cytoplasm
  • Cytoplasm
  • Cytoskeleton
  • Microtubule organizing center
  • Centrosome

Alternative names

  • Coiled-coil domain-containing protein 8
  • CCDC8

Target type

Proteins

Molecular weight

59374Da