CCS
Function
Delivers copper to copper zinc superoxide dismutase (SOD1).
Post-translational modifications
Ubiquitinion by XIAP/BIRC4 leads to enhancement of its chaperone activity toward its physiologic target, SOD1, rather than proteasomal degradation. XIAP/BIRC4 preferentially ubiquitinates at Lys-241.
Sequence Similarities
In the C-terminal section; belongs to the Cu-Zn superoxide dismutase family.
Tissue Specificity
Ubiquitous.
Cellular localization
- Cytoplasm
Alternative names
Copper chaperone for superoxide dismutase, Superoxide dismutase copper chaperone, CCS