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Dab1

Domain

The PID domain specifically binds to the Asn-Pro-Xaa-Tyr(P) motif found in many tyrosine-phosphorylated proteins.

Function

Adapter molecule functioning in neural development. May regulate SIAH1 activity.

Involvement in disease

Spinocerebellar ataxia 37

SCA37

A form of spinocerebellar ataxia, a clinically and genetically heterogeneous group of cerebellar disorders. Patients show progressive incoordination of gait and often poor coordination of hands, speech and eye movements, due to degeneration of the cerebellum with variable involvement of the brainstem and spinal cord. SCA37 is an autosomal dominant form characterized by adult-onset of slowly progressive gait instability, frequent falls, and dysarthria associated with cerebellar atrophy on brain imaging.

None

The disease is caused by variants affecting the gene represented in this entry.

Post-translational modifications

Phosphorylated on Tyr-198 and Tyr-220 upon reelin induction in embryonic neurons. Also phosphorylated on Ser-524 independently of reelin signaling.

Tissue specificity

Mainly expressed in brain.

Alternative names

  • Disabled homolog 1
  • DAB1

Target type

Proteins

Molecular weight

63775Da