DEGS2
Function
Bifunctional enzyme which acts both as a sphingolipid delta(4)-desaturase and a sphingolipid C4-monooxygenase.
Pathway
Membrane lipid metabolism; sphingolipid biosynthesis.
Sequence Similarities
Belongs to the fatty acid desaturase type 1 family. DEGS subfamily.
Tissue Specificity
Highly expressed in skin, intestine and kidney.
Cellular localization
- Endoplasmic reticulum membrane
- Multi-pass membrane protein
Alternative names
C14orf66, DEGS2, Sphingolipid delta(4)-desaturase/C4-monooxygenase DES2, Degenerative spermatocyte homolog 2, Sphingolipid 4-desaturase, Sphingolipid C4-monooxygenase