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Dsp

Developmental stage

Expressed in keratinocytes of newborn mice (at protein level).

Domain

The N-terminal region is required for localization to the desmosomal plaque and interacts with the N-terminal region of PKP1.

Function

Major high molecular weight protein of desmosomes. Regulates profibrotic gene expression in cardiomyocytes via activation of the MAPK14/p38 MAPK signaling cascade and increase in TGFB1 protein abundance (By similarity).

Sequence Similarities

Belongs to the plakin or cytolinker family.

Tissue Specificity

Expressed in undifferentiated keratinocytes of the epidermis at birth, expression increases as differentiation proceeds (at protein level) (PubMed:18079750, PubMed:27375112). Abundantly expressed in the suprabasal layers and weakly in the basal layers of the outer hair root sheath (at protein level) (PubMed:18079750). Expressed at intercalated disks in cardiomyocytes (at protein level) (PubMed:26403541).

Cellular localization

Alternative names

Desmoplakin, DP

swissprot:E9Q557