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EBF3

Function

Transcriptional activator (PubMed:28017370, PubMed:28017372, PubMed:28017373). Recognizes variations of the palindromic sequence 5'-ATTCCCNNGGGAATT-3' (By similarity).

Involvement in disease

Hypotonia, ataxia, and delayed development syndrome

HADDS

An autosomal dominant neurodevelopmental syndrome characterized by global developmental delay, moderate to severe intellectual disability, cerebellar ataxia, hypotonia, speech delay, variable dysmorphic features, and genitourinary abnormalities including vesicoureteric reflux.

None

The disease is caused by variants affecting the gene represented in this entry.

Sequence Similarities

Belongs to the COE family.

Tissue Specificity

Expressed in brain.

Cellular localization

Alternative names

COE3, EBF3, Transcription factor COE3, Early B-cell factor 3, Olf-1/EBF-like 2, EBF-3, O/E-2, OE-2

swissprot:Q9H4W6 entrezGene:253738 omim:607407