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FOXD3

Developmental stage

In spleen levels are higher in adult than in fetal tissue.

Function

Binds to the consensus sequence 5'-A[AT]T[AG]TTTGTTT-3' and acts as a transcriptional repressor (PubMed:11891324). Also acts as a transcriptional activator (PubMed:11891324). Negatively regulates transcription of transcriptional repressor RHIT/ZNF205 (PubMed:22306510). Promotes development of neural crest cells from neural tube progenitors (PubMed:11891324). Restricts neural progenitor cells to the neural crest lineage while suppressing interneuron differentiation (PubMed:11891324). Required for maintenance of pluripotent cells in the pre-implantation and peri-implantation stages of embryogenesis (PubMed:11891324).

Involvement in disease

Autoimmune disease 1

AIS1

An autoimmune disorder characterized by the association of vitiligo with autoimmune thyroiditis (Hashimoto thyroiditis).

None

Disease susceptibility is associated with variants affecting the gene represented in this entry.

Tissue Specificity

Expressed in chronic myeloid leukemia, Jurkat T-cell leukemia and teratocarcinoma cell lines, but not in any other cell lines or normal tissues examined.

Cellular localization

Alternative names

HFH2, FOXD3, Forkhead box protein D3, HNF3/FH transcription factor genesis

swissprot:Q9UJU5 omim:611539 entrezGene:27022