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Glycerol-3-phosphate dehydrogenase [NAD(+)], cytoplasmic

Function

Has glycerol-3-phosphate dehydrogenase activity.

Involvement in disease

Hypertriglyceridemia, transient infantile

HTGTI

An autosomal recessive disorder characterized by onset of moderate to severe transient hypertriglyceridemia in infancy that normalizes with age. The hypertriglyceridemia is associated with hepatomegaly, moderately elevated transaminases, persistent fatty liver, and the development of hepatic fibrosis.

None

The disease is caused by variants affecting the gene represented in this entry.

Sequence Similarities

Belongs to the NAD-dependent glycerol-3-phosphate dehydrogenase family.

Tissue Specificity

Expressed in liver (at protein level).

Cellular localization

Alternative names

GPD-C, GPDH-C, GPD1

swissprot:P21695 entrezGene:2819 omim:138420