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Guanine nucleotide-binding protein subunit beta-5

Function

Enhances GTPase-activating protein (GAP) activity of regulator of G protein signaling (RGS) proteins, such as RGS7 and RGS9, hence involved in the termination of the signaling initiated by the G protein coupled receptors (GPCRs) by accelerating the GTP hydrolysis on the G-alpha subunits, thereby promoting their inactivation (PubMed:27677260). Increases RGS7 GTPase-activating protein (GAP) activity, thereby regulating mood and cognition (By similarity). Increases RGS9 GTPase-activating protein (GAP) activity, hence contributes to the deactivation of G protein signaling initiated by D(2) dopamine receptors (PubMed:27677260). May play an important role in neuronal signaling, including in the parasympathetic, but not sympathetic, control of heart rate (By similarity).

Involvement in disease

Lodder-Merla syndrome, type 1, with impaired intellectual development and cardiac arrhythmia

LDMLS1

An autosomal recessive multisystem disorder characterized by delayed psychomotor development, severe intellectual disability with poor or absent speech, and bradycardia and/or cardiac sinus arrhythmias. Additional features include visual abnormalities, seizures, hypotonia, and gastric reflux.

None

The disease is caused by variants affecting the gene represented in this entry.

Lodder-Merla syndrome, type 2, with developmental delay and with or without cardiac arrhythmia

LDMLS2

An autosomal recessive neurodevelopmental disorder characterized by speech impairment and variable expressivity of attention deficit-hyperactivity disorder. Some patients manifest developmental and motor delay, hypotonia, and sinus-node dysfunction.

None

The disease is caused by variants affecting the gene represented in this entry.

Sequence Similarities

Belongs to the WD repeat G protein beta family.

Tissue Specificity

Widely expressed.

Cellular localization

Alternative names

Guanine nucleotide-binding protein subunit beta-5, Gbeta5, Transducin beta chain 5, GNB5

swissprot:O14775 omim:604447 entrezGene:10681