Skip to main content

Domain

C2H2-type 5 and C2H2-type 6 mediate homodimerization and heterodimerization.

Function

Transcription factor that plays an important role in the regulation of lymphocyte differentiation. Plays an essential role in regulation of B-cell differentiation, proliferation and maturation to an effector state. Involved in regulating BCL2 expression and controlling apoptosis in T-cells in an IL2-dependent manner.

Involvement in disease

Immunodeficiency 84

IMD84

An autosomal recessive immunologic disorder characterized by recurrent sinopulmonary infections from childhood associated with low levels of B cells and impaired early B-cell development. There may also be variable T-cell abnormalities. Patients have increased susceptibility to infection with Epstein-Barr virus and a propensity for the development of lymphoma in adulthood.

None

The disease is caused by variants affecting the gene represented in this entry.

Post-translational modifications

Phosphorylation on tyrosine residues induced by IL2 is required for dissociation from HRAS and nuclear translocation of IKZF3 in T-cells. Phosphorylation on tyrosine residues induced by IL4 is required for dissociation from Bcl-X(L) in T-cells.

Sequence similarities

Belongs to the Ikaros C2H2-type zinc-finger protein family.

Tissue specificity

Expressed most strongly in peripheral blood leukocytes, the spleen, and the thymus.

Cellular localization

  • Nucleus
  • Cytoplasm
  • Isoform 1
  • Nucleus
  • Isoform 3
  • Nucleus
  • Isoform 11
  • Nucleus
  • Isoform 14
  • Nucleus
  • Cytoplasm
  • Isoform 12
  • Cytoplasm

Alternative names

ZNFN1A3, IKZF3, Zinc finger protein Aiolos, Ikaros family zinc finger protein 3

Target type

Proteins

Molecular weight

58023Da

We found 12 products in 2 categories

Primary Antibodies

Proteins & Peptides

Target

Species of origin