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Mitochondrial inner membrane protein OXA1L

Function

Mitochondrial membrane insertase that mediates the cotranslational insertion of integral membrane proteins into the mitochondrial inner membrane (PubMed:17936786, PubMed:33602856, PubMed:7991568). Essential for the activity and assembly of cytochrome oxidase (PubMed:17936786, PubMed:7991568). Required for the correct biogenesis of ATP synthase and complex I in mitochondria (PubMed:17936786, PubMed:7991568).

Sequence Similarities

Belongs to the OXA1/ALB3/YidC family.

Cellular localization

Alternative names

Mitochondrial inner membrane protein OXA1L, OXA1Hs, Oxidase assembly 1-like protein, OXA1-like protein, OXA1L

swissprot:Q15070 entrezGene:5018 omim:601066