MTX1
Function
Involved in transport of proteins into the mitochondrion. Essential for embryonic development (By similarity).
Post-translational modifications
Ubiquitinated by PRKN during mitophagy, leading to its degradation and enhancement of mitophagy. Deubiquitinated by USP30.
Sequence Similarities
Belongs to the metaxin family.
Cellular localization
- Membrane
- Single-pass type I membrane protein
- Mitochondrion outer membrane
Alternative names
MTX, MTXN, MTX1, Metaxin-1, Mitochondrial outer membrane import complex protein 1