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RGR

Function

Receptor for all-trans- and 11-cis-retinal. Binds preferentially to the former and may catalyze the isomerization of the chromophore by a retinochrome-like mechanism.

Involvement in disease

Retinitis pigmentosa 44

RP44

A retinal dystrophy belonging to the group of pigmentary retinopathies. Retinitis pigmentosa is characterized by retinal pigment deposits visible on fundus examination and primary loss of rod photoreceptor cells followed by secondary loss of cone photoreceptors. Patients typically have night vision blindness and loss of midperipheral visual field. As their condition progresses, they lose their far peripheral visual field and eventually central vision as well.

None

The disease is caused by variants affecting the gene represented in this entry.

Post-translational modifications

Covalently binds all-trans- and 11-cis-retinal.

Sequence Similarities

Belongs to the G-protein coupled receptor 1 family. Opsin subfamily.

Tissue Specificity

Preferentially expressed at high levels in the retinal pigment epithelium (RPE) and Mueller cells of the neural retina.

Cellular localization

Alternative names

RPE-retinal G protein-coupled receptor, RGR

swissprot:P47804 omim:600342 entrezGene:5995