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Function

Has a role in alternative splicing and transcription regulation (PubMed:29522154). Involved in both constitutive and alternative pre-mRNA splicing. May have a role in the recognition of the 3' splice site during the second step of splicing.

Involvement in disease

Intellectual developmental disorder, autosomal recessive 70

MRT70

A form of intellectual disability, a disorder characterized by significantly below average general intellectual functioning associated with impairments in adaptive behavior and manifested during the developmental period. MRT70 patients manifest impaired intellectual development, mild facial dysmorphism, febrile seizures, and behavioral abnormalities.

None

The disease is caused by variants affecting the gene represented in this entry.

Post-translational modifications

Phosphorylated.

Tissue specificity

Widely expressed. Expressed in brain, spinal cord, cerebellum.

Cellular localization

  • Nucleus
  • Nucleus speckle
  • Cytoplasm
  • Shuttles between the nucleus and cytoplasm.

Alternative names

SRRP53, BM-011, RSRC1, Serine/Arginine-related protein 53, SRrp53, Arginine/serine-rich coiled-coil protein 1

Target type

Proteins

Molecular weight

38677Da

We found 1 product in 1 category

Primary Antibodies

Target

Application

Reactive species

Search our catalogue for 'RSRC1' (1)

Products