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SOD1

Function

Destroys radicals which are normally produced within the cells and which are toxic to biological systems.

Post-translational modifications

Palmitoylation helps nuclear targeting and decreases catalytic activity.

Succinylation, adjacent to copper catalytic site, probably inhibits activity. Desuccinylation by SIRT5 enhances activity.

Sequence Similarities

Belongs to the Cu-Zn superoxide dismutase family.

Cellular localization

Alternative names

Superoxide dismutase [Cu-Zn], SOD1

swissprot:P00442 entrezGene:281495