Skip to main content

Function

Important for the control of mitochondrial reactive oxygen species homeostasis, apoptosis regulation and cell viability. Possesses a dithiol-reducing activity.

Involvement in disease

Combined oxidative phosphorylation deficiency 29

COXPD29

An autosomal recessive, infantile-onset, neurodegenerative disorder characterized by decreased activities of mitochondrial respiratory complexes I and III, severe cerebellar atrophy, epilepsy, dystonia, optic atrophy, and peripheral neuropathy.

None

The disease is caused by variants affecting the gene represented in this entry.

Sequence similarities

Belongs to the thioredoxin family.

Tissue specificity

Widely expressed in adult (at protein level) and fetal tissues.

Cellular localization

  • Mitochondrion

Alternative names

TRX2, TXN2, MTRX, Mt-Trx, Thioredoxin-2

Target type

Proteins

Primary research area

Metabolism

Molecular weight

18383Da