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VARS1

Function

Catalyzes the attachment of valine to tRNA(Val).

Involvement in disease

Neurodevelopmental disorder with microcephaly, seizures, and cortical atrophy

NDMSCA

An autosomal recessive neurodevelopmental disorder characterized by severe developmental delay, intellectual disability, severe microcephaly, and cortical atrophy.

None

The disease may be caused by variants affecting the gene represented in this entry.

Sequence Similarities

Belongs to the class-I aminoacyl-tRNA synthetase family.

Alternative names

G7A, VARS, VARS2, VARS1, Valine--tRNA ligase, Protein G7a, Valyl-tRNA synthetase, ValRS

swissprot:P26640 omim:192150 entrezGene:7407